Sfoglia per Autore
Mutant PrP is delayed in its exit from the endoplasmic reticulum, but neither wild-type nor mutant PrP undergoes retrotranslocation prior to proteasomal degradation
2003-01-01 Drisaldi, Bettina; Stewart, Richard S.; Adles, Cheryl; Stewart, Leanne R.; Quaglio, Elena; Biasini, Emiliano; Fioriti, Luana; Chiesa, Roberto; Harris, David A.
Proteasome inhibition and aggregation in Parkinson's disease: A comparative study in untransfected and transfected cells
2004-01-01 Biasini, Emiliano; Fioriti, Luana; Ceglia, Ilaria; Invernizzi, Roberto; Bertoli, Alessandro; Chiesa, Roberto; Forloni, Gianluigi
Analysis of the cerebellar proteome in a transgenic mouse model of inherited prion disease reveals preclinical alteration of calcineurin activity
2006-01-01 Biasini, Emiliano; Massignan, Tania; Fioriti, Luana; Rossi, Valentina; Dossena, Sara; Salmona, Mario; Forloni, Gianluigi; Bonetto, Valentina; Chiesa, Roberto
Redox regulation of cyclophilin A by glutathionylation
2006-01-01 Ghezzi, Pietro; Casagrande, Simona; Massignan, Tania; Basso, Manuela; Bellacchio, Emanuele; Mollica, Luca; Biasini, Emiliano; Tonelli, Rossella; Eberini, Ivano; Gianazza, Elisabetta; Dai, Wei Wei; Fratelli, Maddalena; Salmona, Mario; Sherry, Barbara; Bonetto, Valentina
Proteomic analysis of spinal cord of presymptomatic amyotrophic lateral sclerosis G93A SOD1 mouse
2007-01-01 Massignan, Tania; Casoni, Filippo; Basso, Manuela; Stefanazzi, Paola; Biasini, Emiliano; Tortarolo, Massimo; Salmona, Mario; Gianazza, Elisabetta; Bendotti, Caterina; Bonetto, Valentina
Human prion proteins with pathogenic mutations share common conformational changes resulting in enhanced binding to glycosaminoglycans
2007-01-01 Yin, Shaoman; Pham, Nancy; Yu, Shuiliang; Li, Chaoyang; Wong, Poki; Chang, Binggong; Kang, Shin Chung; Biasini, Emiliano; Tien, Po; Harris, David A.; Sy, Man Sun
Multiple biochemical similarities between infectious and non-infectious aggregates of a prion protein carrying an octapeptide insertion
2008-01-01 Biasini, Emiliano; Medrano, Andrea Z.; Thellung, Stefano; Chiesa, Roberto; Harris, David A.
GFP-tagged mutant prion protein forms intra-axonal aggregates in transgenic mice
2008-01-01 Medrano, Andrea Z.; Barmada, Sami J.; Biasini, Emiliano; Harris, David A.
Aggregated, wild-type prion protein causes neurological dysfunction and synaptic abnormalities
2008-01-01 Chiesa, Roberto; Piccardo, Pedro; Biasini, Emiliano; Ghetti, Bernardino; Harris, David A.
Non-infectious aggregates of the prion protein react with several PrP Sc-directed antibodies
2008-01-01 Biasini, Emiliano; Seegulam, M. Esa; Patti, Brianna N.; Solforosi, Laura; Medrano, Andrea Z.; Christensen, Heather M.; Senatore, Assunta; Chiesa, Roberto; Williamson, R. Anthony; Harris, David A.
Immunopurification of pathological prion protein aggregates
2009-01-01 Biasini, Emiliano; Tapella, Laura; Mantovani, Susanna; Stravalaci, Matteo; Gobbi, Marco; Harris, David A.; Chiesa, Roberto
The hydrophobic core region governs mutant prion protein aggregation and intracellular retention
2010-01-01 Biasini, Emiliano; Tapella, Laura; Restelli, Elena; Pozzoli, Manuela; Massignan, Tania; Chiesa, Roberto
Synthetic amyloid-β oligomers impair long-term memory independently of cellular prion protein
2010-01-01 Balducci, Claudia; Beeg, Marten; Stravalaci, Matteo; Bastone, Antonio; Sclip, Alessandra; Biasini, Emiliano; Tapella, Laura; Colombo, Laura; Manzoni, Claudia; Borsello, Tiziana; Chiesa, Roberto; Gobbi, Marco; Salmona, Mario; Forloni, Gianluigi
Mutant prion protein expression is associated with an alteration of the rab GDP dissociation inhibitor α (GDI)/rab11 pathway
2010-01-01 Massignan, Tania; Biasini, Emiliano; Lauranzano, Eliana; Veglianese, Pietro; Pignataro, Mauro; Fioriti, Luana; Harris, David A.; Salmona, Mario; Chiesa, Roberto; Bonetto, Valentina
A novel, drug-based, cellular assay for the activity of neurotoxic mutants of the prion protein
2010-01-01 Massignan, Tania; Stewart, Richard S.; Biasini, Emiliano; Solomon, Isaac H.; Bonetto, Valentina; Chiesa, Roberto; Harris, David A.
The N-terminal, polybasic region is critical for prion protein neuroprotective activity
2011-01-01 Turnbaugh, Jessie A.; Westergard, Laura; Unterberger, Ursula; Biasini, Emiliano; Harris, David A.
A Drug-Based Cellular Assay (DBCA) for studying cytotoxic and cytoprotective activities of the prion protein: A practical guide
2011-01-01 Massignan, Tania; Biasini, Emiliano; Harris, David A.
An N-terminal polybasic domain and cell surface localization are required for mutant prion protein toxicity
2011-01-01 Solomon, Isaac H.; Khatri, Natasha; Biasini, Emiliano; Massignan, Tania; Huettner, James E.; Harris, David A.
Targeting the cellular prion protein to treat neurodegeneration
2012-01-01 Biasini, Emiliano; Harris, David A.
The toxicity of a mutant prion protein is cell-autonomous, and can be suppressed by wild-type prion protein on adjacent cells
2012-01-01 Biasini, Emiliano; Turnbaugh, Jessie A.; Massignan, Tania; Veglianese, Pietro; Forloni, Gianluigi; Bonetto, Valentina; Chiesa, Roberto; Harris, David A.
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